An infant often has seizures and he has increased size of the liver. There are elevated levels of lactate and pyruvate and hypoglycemia in the blood. With injection of adrenaline glucose in the blood does not increase; the amount of lactic acid increases. Liver biopsy revealed a reduced activity of glucose-6-phosphatase. Your probable diagnosis:

(Your probable diagnosis)Girke disease

glucose-6-phosphate to glucose