Hunter syndrome is mucopolysaccharidosis type II. It is manifested by bone deformations, hearing loss, oligophrenia, changes in the ocular fundus. In addition, there is an increased urinary output of dermatan- and heparan sulfates.
What are the reasons for mucopolysaccharidosis developmentdisorder of GAG catabolism in
lysosome
What types of GAG do you know chondroetin -4-sulphate-, chondroetin
-6-sulphate-,heparin,keratan-sulphate,hyulonoronic acid,dermatan-sulphate.
What is the structure of heparan sulfate Consist of glucuronic acid linked to n-acetylglucosamide
What are the functions of heparan sulfate in structure of basemembrane (kidney)
What are proteoglycansCompound
consist of pprotein bounded to mucopolysacchride
What is the structure of proteoglycanscore protein bind with gag
What are the functions
of proteoglycans? included
in binding cation,
Thery form large compound
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